A CLINICAL CASE OF NECROTIZING SCLERITIS ASSOCIATED WITH WEGENE R’S GRANULOMATOSIS DETECTED FOR THE FIRST TIME IN OPHTHALMOLOGICAL PRACTICE

Granulomatosis with polyangiitis (GPA or Wegener's granulomatosis) is a rare systemic autoimmune disease of unknown etiology characterized by granulomatous inflammation, tissue necrosis, and vasculitis of small to medium-sized vessels. Respiratory tract involvement is the most common, affecting up to 85% of patients, followed by the renal system in 75% of patients, with Wegener's granulomatosis ocular involvement estimated to occur in 50 – 60% of patients. Damage to the organ of vision can not only significantly reduce the quality of life of the patient, but in rare cases lead to severe complications, including death. The article describes a clinical case of a 51-year-old woman who suffered from end-stage chronic kidney disease, polysegmental pneumonia with signs of destruction and necrotizing scleritis.

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